Hyperammonaemia

Also known as: Hyperammonemia / Disorder of urea cycle metabolism, unspecified / Hyperammonemia (disorder)

DrugDrug NameDrug Description
DB00125ArginineAn amino acid commonly found as a component of total parenteral nutrition.
DB13207Arginine glutamateTwo amino acids indicated in the treatment of hyperammonemia and in combination for total parenteral nutrition.
DB09269Phenylacetic acidAn agent used as an adjunct to treat acute hyperammonemia and associated encephalopathy in adult and pediatric patients with deficiencies in enzymes of the urea cycle.
DB15819Potassium aspartateA potassium supplement used to treat hypokalemia or hyperammonemia.
DrugDrug NamePhaseStatusCount
DB06819Phenylbutyric acid1Terminated1
DB15447Setogepram1Terminated1
DB16312TNP-20921Completed1
DB16312TNP-20921 / 2Completed1
DB06775Carglumic acidNot AvailableEnrolling by Invitation1
DB06775Carglumic acidNot AvailableRecruiting1